Aortopulmonary window
Aortopulmonary window refers to a congenital heart defect similar in some ways to persistent truncus arteriosus.[2] Persistent truncus arteriosus involves a single valve; aortopulmonary window is a septal defect.[3]
| Aortopulmonary window | |
|---|---|
| Other names | Aortopulmonary septal defect[1] |
| Specialty | Medical genetics  |
A large number of patients with a large APW usually die within 1 year of age. It is extremely rare to find cases of APW surviving till adult age and it is still rare to surgically treat such patients who are incidentally detected in adult age because such subsets of patients invariably have associated pulmonary vascular obstructive disease in advanced stage and thus there is therapeutic dilemma to surgically correct these patients.Although cases of uncorrected AP window presenting in adulthood have been reported but literature on surgically treated AP window in adult populations is limited. A rare case of successful surgical management of an incidentally detected large aortopulmonary window with reversible pulmonary arterial hypertension has been reported as isolated case reports. [4]
See also
References
- "Aortopulmonary window: MedlinePlus Medical Encyclopedia". medlineplus.gov. Retrieved 27 May 2019.
- Stevenson, Roger E.; Hall, Judith G. (2006). Human malformations and related anomalies. Oxford University Press US. pp. 119–. ISBN 978-0-19-516568-5. Retrieved 19 July 2011.
- Donoghue, Veronica B.; Bjørnstad, Per G. (2007-11-29). Radiological Imaging of the Neonatal Chest. Springer. pp. 330–. ISBN 978-3-540-33748-5. Retrieved 19 July 2011.
- Khanna, Sudhansoo; Mahajan, Sachin; Halder, Vikram; Gowda, Nischitha (2020-04-19). "Incidental diagnosis of a large aortopulmonary window with reversible pulmonary arterial hypertension in adult age and its surgical management". Journal of Cardiac Surgery. doi:10.1111/jocs.14569. ISSN 0886-0440.