Indian childhood cirrhosis
Indian childhood cirrhosis is a chronic liver disease of childhood characterised by cirrhosis of the liver[1] due to deposition of copper in the liver.[2] It primarily affects children of 1–3 years of age and has a genetic predisposition. It had a very high case fatality in the past[3] but has eventually become preventable, treatable and is now rare.[4]
Variants
- North American Indian childhood cirrhosis [5]
References
- Editorial (August 2008). "Indian childhood cirrhosis: Several dilemmas resolved" (PDF). Indian J Med Res. 128 (2): 93–96. PMID 19001668.
- Tanner, MS (May 1998). "Role of copper in Indian childhood cirrhosis". The American Journal of Clinical Nutrition. 67 (5 Suppl): 1074S–1081S. doi:10.1093/ajcn/67.5.1074S. PMID 9587155.
- Nayak, NC; et al. "Indian childhood cirrhosis-A reevaluation of its pathognomonic features and their significance in the light of clinical data and natural history of the disease" (PDF). Cite journal requires
|journal=(help) - Pandit, A; Bhave, S (May 1996). "Present interpretation of the role of copper in Indian childhood cirrhosis". The American Journal of Clinical Nutrition. 63 (5): 830S–5S. doi:10.1093/ajcn/63.5.830. PMID 8615370.
- Richter, A; Mitchell, GA; Rasquin, A (Nov 2007). "[North American Indian childhood cirrhosis (NAIC)]". Médecine/Sciences. 23 (11): 1002–7. doi:10.1051/medsci/200723111002. PMID 18021715.
Further reading
- North American Indian childhood cirrhosis on Genetics Home Reference
- Paton, A (October 17, 1981). "Indian childhood cirrhosis". Br Med J (Clin Res Ed). 283 (6298): 1006. doi:10.1136/bmj.283.6298.1006. PMC 1507261. PMID 6794739.
- Raju, VB; Sundaravalli, N; Sriramachari, S (Nov–Dec 1980). "Indian childhood cirrhosis: clinical features, prognosis and treatment". Indian Journal of Pediatrics. 47 (389): 537–41. doi:10.1007/BF02822546. PMID 7262970. S2CID 30670129.
- Bavdekar, AR; Bhave, SA; Pradhan, AM; Pandit, AN; Tanner, MS (1996). "Long term survival in Indian childhood cirrhosis treated with D-penicillamine". Archives of Disease in Childhood. 74 (1): 32–35. doi:10.1136/adc.74.1.32. PMC 1511595. PMID 8660042.
- Nayak N.C.; Chitale A.R. (2013). "Indian childhood cirrhosis (ICC) & ICC-like diseases: The changing scenario of facts versus notions". Indian J. Med. Res. 137 (6): 1029–42. PMC 3734708. PMID 23852284.
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